Renal Epithelioid Angiomyolipoma: Successfully Treated With Chemotherapy

Renal epithelioid angiomyolipoma (REA) is a rare mesenchymal tumor. The primary choice of treatment is local treatments. There is no consensus about adjuvant treatment. Doxorubicine, dacarbazine, ifosfamide, cyclophosphamide and cisplatin were shown to be effective in some case reports We present a metastatic renal epithelioid angiomyolipoma case that was treated with doxorubicin in the first line and combination of cisplatin and dacarbazine therapies in the second line. Best response to these two regimens was stable disease. First choice of therapy is surgery if feasible. We did not get clinical response with doxorubicin, cisplatin, and dacarbazine. Therefore, we need new agents for treating these patients.